가족성 선종성 용종증 수술 후 발생한 복강 내 유건종 1예 |
정인두·방성조·신정우·박능화·최대화*·차희정†·김도하 |
울산대학교 의과대학 울산대학교병원 내과, *외과, †병리과 |
A Case of Intra-abdominal Desmoid Tumor after Total Colectomy in a Patient with Familial Adenomatous Polyposis |
In Du Jeong, M.D., Sung Jo Bang, M.D., Jung Woo Shin, M.D., Neung Hwa Park, M.D., Dae Hwa Choi, M.D.*, Hee Jeong Cha, M.D.† and Do Ha Kim, M.D. |
Departments of Internal Medicine, *Surgery and †Pathology, Ulsan University Hospital, University of Ulsan College of Medicine, Ulsan, Korea |
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Abstract |
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Familial adenomatous polyposis (FAP) arises from germline mutations of the adenomatous polyposis coli (APC) gene. FAP is characterized by the occurrence of hundreds to thousands of adenomas throughout the colorectum, and there is nearly a 100% risk of colorectal cancer. In addition to polyposis coli, patients with FAP can develop a variety of extracolonic manifestations. Recent advances in screening and surgery have reduced the colon cancer occurrence and death in FAP patients, leaving desmoid tumors as a leading cause of their morbidity and mortality. Treatment of desmoid tumors is generally considered to be challenging for both the doctor and the patient. We report here on an 18 year old man with resectable intra-abdominal desmoid tumor that developed after total colectomy due to FAP and we include a review of the relevant literature. (Korean J Gastrointest Endosc 2006;33:5053) |
Key Words:
Familial adenomatous polyposis, Desmoid tumor |
주요어:
가족성 선종성 용종증, 유건종 |
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