Korean Journal of Gastrointestinal Endoscopy 2008;36(4): 252-255.
선천적 등쪽 췌장 완전 발육 부전증 1예
김선정ㆍ한병훈ㆍ정현주ㆍ유홍준ㆍ양성우ㆍ박세영ㆍ이상욱
고신대학교 의과대학 내과학교실
A Case of Complete Agenesis of the Dorsal Pancreas
Sun Jung Kim, M.D., Byung Hoon Han, M.D., Hyun Joo Jung, M.D., Hong Jun You, M.D., Sung Woo Yang, M.D., Se Young Park, M.D. and Sang Uk Lee, M.D.
Department of Internal Medicine, Kosin University College of Medicine, Busan, Korea
Abstract
The pancreas with the complete absence of its body and tail is the result of underdevelopment or agenesis of the dorsal pancreatic bud during embryogenesis, and this is a rare anomaly. We report here on a case of a 38-year-old man who had a pancreas with the total absence of the body and tail. On the abdominal computed tomography (CT), only a pancreatic head portion with speckled calcifications was seen, and the pancreatic body and tail were not visualized at all. Endoscopic retrograde cholangiopancreatography (ERCP) showed only a short major pancreatic duct with smooth tapering and terminal arborization. The Ampulla of Vater had a normal appearance and it was located at the medial side of the second portion of the duodenum. There was no difficulty to perform cannulation. Any minor papilla was not found. On magnetic resonance cholangiopancreatography (MRCP), the duct of Santorini and the duct in the body and tail were not visualized. (Korean J Gastrointest Endosc 2008;36:252-256)