Korean J Gastrointest Endosc > Volume 37(5); 2008 > Article
Korean Journal of Gastrointestinal Endoscopy 2008;37(5): 384-388.
von Hippel-Lindau병 환자의 이중 비르숭관 췌장 1예
김혜수ㆍ한병훈ㆍ김선정ㆍ이지숙ㆍ박세진ㆍ이상욱ㆍ허방*ㆍ김정현
고신대학교 의과대학 내과학교실, *병리학교실, 성균관대학교 의과대학 삼성서울병원 진단검사의학교실
A Case of Pancreatic Dual Wirsung Ducts in a Patient with von Hippel-Lindau Disease
Hye Soo Kim, M.D., Byung Hoon Han, M.D., Sun Jung Kim, M.D., Jee Sook Lee, M.D., Sae Jin Park, M.D., Sang Uk Lee, M.D., Bang Hur, M.D.* and Jung Hyun Kim, M.D.
Departments of Internal Medicine and *Pathology, Kosin University College of Medicine, Busan, Department of Laboratory Medicine, Samsung Medical Center, Sungkyunkwan University School of Medicine, Seoul, Korea
Abstract
Rare autosomal dominant disorders associated with various tumors and cysts, and several kinds of pancreatic lesions have been described in patients with von Hippel- Lindau (VHL) disease, but there have been few studies concerned with the variations of the pancreatic duct. We experienced a case of pancreatic dual Wirsung ducts in a patient with VHL disease. Computed tomography scans showed that multiple cysts had nearly completely replaced the pancreas, there was a solid tumor on the uncinate process of the pancreas and a left renal mass suggested renal cell carcinoma. ERCP shows that the Santorini duct and Wirsung duct were fused in a normal fashion, and another Wirsung duct had shrub-like branches that are commonly seen in pancreatic divisum. (Korean J Gastrointest Endosc 2008;37:384-388)
Key Words: von Hippel-Lindau disease, Pancreas, Pancreatic duct, Dual Wirsung ducts
주요어: von Hippel-Lindau병, 췌장, 췌장관, 이중 비르숭관
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