내시경적 밴드 결찰술과 용종 절제술로 치료한 Blue Rubber Bleb Nevus Syndrome 1예 |
배선윤ㆍ김진용ㆍ윤원경ㆍ정호중ㆍ김미연ㆍ이미래ㆍ황지원 |
성균관대학교 의과대학 삼성서울병원 내과학교실 |
A Case of Blue Rubber Bleb Nevus Syndrome Treated by Endoscopic Band Ligation and Endoscopic Polypectomy |
Sun Youn Bae, M.D., Jin Yong Kim, M.D., Won Kyung Yun, M.D., Ho Jung Chung, M.D., Mi Yeon Kim, M.D., Mi Rae Lee, M.D. and Ji Won Hwang, M.D. |
Department of Medicine, Samsung Medical Center, Sungkyunkwan University School of Medicine, Seoul, Korea |
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Abstract |
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Blue rubber bleb nevus syndrome (BRBNS) is a rare disorder that is characterized by multiple cutaneous vascular malformations in the skin and gastrointestinal tract and is associated with intestinal hemorrhage and iron deficiency anemia. This syndrome may induce severe or fatal bleeding; however, the causes of this syndrome are unknown. We report here a case of BRBNS that was diagnosed in a 20-year-old male with chronic anemia and a past history of surgery due to cutaneous hemangioma on the shoulder and thigh. One purplish hemangioma on the stomach and multiple bluish hemangiomas on the colon were noted on the endoscopic examination. We successfully treated the GI hemangioma with endoscopic band ligation and endoscopic polypectomy. (Korean J Gastrointest Endosc 2009;39:304-307) |
Key Words:
Blue rubber bleb nevus syndrome, Anemia, Hemangioma |
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